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| 1 | Primary intestinal lymphangiectasia in an adult patient:A case report and review of literature显示文摘BACKGROUND Primary intestinal lymphangiectasia(PIL),first described in 1961,is a rare disorder of unknown etiology resulting in protein-losing enteropathy.The disease is characterized by dilatation and leakage of intestinal lymph vessels leading to hypoalbuminemia,hypogammaglobulinemia,and lymphopenia.Since the severity and location of lymph vessels being affected can vary considerably,the range of associated symptoms is wide from mild lower-limb edema to generalized edema,abdominal and/or pleural effusion,and recurrent diarrhea,among others.Although usually developing in early childhood,we present the case of a 34-yearold woman with PIL.Moreover,we performed a literature review systematically assessing clinical presentation,and provide a practical approach to facilitate diagnosis and therapy of PIL in adults.CASE SUMMARY Our patient presented with unspecific symptoms of abdominal discomfort,fatigue,nausea,and recurrent edema of the lower limbs.Interestingly,a striking collinearity of clinical symptoms with female hormone status was evident.Additionally,polyglobulia,hypoalbuminemia,hypogammaglobulinemia,and transient lymphocytopenia were evident.Due to suspicion of a bone marrow disease,an extensive diagnostic investigation was carried out excluding secondary causes of polyglobulinemia and hypoalbuminemia.The diagnosis of primary intestinal lymphangiectasia was established after 22 wk by histological analysis of biopsy samples obtained via enteroscopy.Consecutively,the patient was put on a high-protein and low-fat diet with medium-chain triglycerides supplementation leading to significant improvement of clinical symptoms until 2 years of follow-up.CONCLUSION PIL can be the reason for cryptogenic hypoalbuminemia,hypogammaglobulinemia,and lymphopenia in adulthood.Due to difficulty in correct diagnosis,treatment initiation is often delayed despite being effective and welltolerated.This leads to a significant disease burden in affected patients.PIL is increasingly been recognized in adults since the majority of case reports were published within the last 10 years,pointing towards an underestimation of the true prevalence.The association with female hormone status warrants further investigation. | Rudolf Huber Georg Semmler Alexander Mayr Felix Offner Christian Datz | 2020 | World Journal of Gastroenterology2020，26，48： | 6 |
| 2 | 生物质和废弃油脂流化床共催化热解实验研究显示文摘本文在连续进料流化床实验台上采用ZSM-5催化剂对生物质和废弃油脂单独催化热解以及共催化热解进行了实验研究。主要考察了反应温度和质量空速对废弃油脂催化热解以及不同有效氢碳比对生物质和废弃油脂共催化热解的影响。结果表明,在温度为550℃、质量空速为0.35h^(-1)时,总化学品(芳香烃+烯烃+C5化合物)碳产率达到最大值(53.9%)。生物质和废弃油脂共催化热解能够大幅提高烯烃和芳香烃的产率,在较高有效氢碳比下(>0.8),丙烯的选择性高达60%。 | 张会岩 肖睿 George W Huber | 2013 | 工程热物理学报2013，34，4： | 5 |
| 3 | Organizational Learning: The Contributing Processes and the Literatures显示文摘 | George P. Huber | 1991 | Organization Science1991，，1： | 5 |
| 4 | Organizational Learning: The Contributing Processes and the Literatures显示文摘 | George P. Huber | 1991 | Organization Science1991，，1： | 2 |
| 5 | Analysis of perfluorooctanoate (PFOA) and other perfluorinated compounds (PFCs) in the River Po watershed in N-Italy显示文摘 | Robert Loos Giovanni Locoro Tania Huber Jan Wollgast Eugen H. Christoph Alfred de Jager Bernd Manfred Gawlik Georg Hanke Gunther Umlauf José-Manuel Zaldívar | 2007 | Chemosphere2007，，2： | 2 |
| 6 | Polar herbicides, pharmaceutical products, perfluorooctanesulfonate (PFOS), perfluorooctanoate (PFOA), and nonylphenol and its carboxylates and ethoxylates in surface and tap waters around Lake Maggiore in Northern Italy显示文摘 | Robert Loos Jan Wollgast Tania Huber Georg Hanke | 2007 | Analytical and Bioanalytical Chemistry2007，，4： | 1 |
| 7 | Organizational Learning: The Contributing Processes and the Literatures 显示文摘 | Huber George P | 1991 | Organization Science1991，，2： | 1 |
| 8 | Organizational learning: The contributing processes and the hteratures显示文摘 | Huber George P | 1991 | Organizational Science1991，2，1： | 1 |
| 9 | Production of liquid alkanes by aqueous-phase processing of biomass-derived carbohydrates显示文摘 | George W Huber Juben N Christopher J Barrett | 2005 | Science2005，308，： | 1 |
| 10 | Synthesis of transportation fuels from biomass: chemistry, catalysts, and engineering显示文摘 | Huber George W Iborra Sara Corma Avelino | 2006 | Chemical Reviews2006，106，9： | 1 |
| 11 | Investigation into the shape selectivity of zeolite catalysts for biomass conversion显示文摘 | Jungho Jae Geoffrey A. Tompsett Andrew J. Foster Karl D. Hammond Scott M. Auerbach Raul F. Lobo George W. Huber | 2011 | Journal of Catalysis2011，，2： | 1 |
| 12 | Synthesis of transportation fuels from biomass: Chemistry, catalysts, and engineering显示文摘 | GEORGE W HUBER SARA IBORRA AVELINO CORMA | 2006 | Chemical Reviews2006，106，9： | 1 |
| 13 | Processing biomass in conventional oil refineries: Production of high quality diesel by hydrotreating vegetable oils in heavy vacuum oil mixtures显示文摘 | George W Huber Paul O'Connor Avelino Corma | 2007 | Applied Catalysis A: General2007，329，： | 1 |
| 14 | Investigation into the shape selectivity of zeolite catalysts for biomass conversion显示文摘 | Jungho Jae Geoffrey A. Tompsett Andrew J. Foster Karl D. Hammond Scott M. Auerbach Raul F. Lobo George W. Huber | 2011 | Journal of Catalysis2011，，2： | 1 |
| 15 | Synthesis of transportation fuels from biomass : chemistry, catalysts, and engineering 显示文摘 | GEORGE W HUBER SARA LBORRA AVELINO CORMA | 2006 | Chemical Re- views2006，106，9： | 1 |
| 16 | Side Effects of Phytoestrogens: A Meta-analysis of Randomized Trials显示文摘 | Clemens B. Tempfer Georg Froese Georg Heinze Eva-Katrin Bentz Lukas A. Hefler Johannes C. Huber | 2009 | The American Journal of Medicine2009，，10： | 1 |
| 17 | An overview of aqueous-phase catalytic processes for production of hydrogen and alkanes in a biorefinery 显示文摘 | George W Huber James A Dumesic | 2006 | Catalysis Today2006，111，： | 1 |
| 18 | Organizational Learning: the Contributing Process and the Literatures 显示文摘 | HUBER GEORGE P | 1991 | Organization Science1991，2，1： | 1 |
| 19 | Synergies between bio-oil refineries for the production of fuels from biomass显示文摘 | GEORGE HUBER PROF AVELINO CORMA PROF | 2007 | General & Introductory Chemistry2007，46，38： | 1 |
| 20 | Organizational Learning: The Contributing Processes and the Literatures显示文摘 | George P. Huber | 1991 | Organization Science1991，，1： | 1 |
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